Vasculitic Syndromes Flashcards
What are some characteristic features of secondary Reynauds
Nail fold capillary abnormalities
Digital pitting or ulceration
Skin tightening
Diminished pulse
What are some features that can differentiate between primary and secondary Reynaud
Primary: symmetric involvement of fingers in both hands; frequent prolonged spasm; no digital pitting/ ulceration
What large vessel vasculitis chiefly affects women during reproductive years and is often found in the aorta and its branches
Takayasu arteritis
What vasculitis affects medium sized arterioles, spares the lungs but often involves the kidney and can present with hand or foot drop, abdominal pain and palpable purpura
Polyarteritis nodosa
What small vessel vasculitis usually has its onset in young adulthood causes recurrent attacks of aphthous ulcers, genital ulcers, uvitis and can cause CNS abnormalities
Behcet syndrome
Common in Turkish, Asian, Middle East
What small vessel vasculitis presents with a triad of upper, lower respiratory tract disease and glomerulonephritis and often affects the gums
Granulomatous polyangitis